{"id":2366,"date":"2020-04-22T13:51:36","date_gmt":"2020-04-22T10:51:36","guid":{"rendered":"https:\/\/annelertoplandik.com\/blog\/?p=2366"},"modified":"2020-04-22T13:51:38","modified_gmt":"2020-04-22T10:51:38","slug":"hirschsprung-hastaligi-nedir","status":"publish","type":"post","link":"https:\/\/annelertoplandik.com\/blog\/hirschsprung-hastaligi-nedir\/","title":{"rendered":"Hirschsprung Hastal\u0131\u011f\u0131 Nedir?"},"content":{"rendered":"\n<p>Hirschsprung hastal\u0131\u011f\u0131, kal\u0131n ba\u011f\u0131rsa\u011f\u0131 (kolon) etkileyen ve d\u0131\u015fk\u0131 ge\u00e7irmede sorunlara neden olan bir durumdur.&nbsp;Durum do\u011fumda (konjenital) bebe\u011fin kal\u0131n ba\u011f\u0131rsak kaslar\u0131ndaki eksik sinir h\u00fccrelerinin bir sonucu olarak ortaya \u00e7\u0131kar.<\/p>\n\n\n\n<p>Hirschsprung hastal\u0131\u011f\u0131 olan bir yenido\u011fan genellikle do\u011fumdan sonraki g\u00fcnlerde ba\u011f\u0131rsak hareketine sahip olamaz.\u00a0Hafif vakalarda, \u00e7ocukluk \u00e7a\u011f\u0131n\u0131n sonlar\u0131na kadar durum tespit edilemeyebilir.\u00a0Nadiren, bu hastal\u0131k ilk olarak yeti\u015fkinlerde te\u015fhis edilir.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Hirschsprung hastal\u0131\u011f\u0131 nedir?<\/strong><\/h2>\n\n\n\n<p>Hirschsprung hastal\u0131\u011f\u0131 konjenital bir kusurdur, yani bir ki\u015fi onunla do\u011far.&nbsp;Bu kusur en yayg\u0131n olarak kal\u0131n ba\u011f\u0131rsa\u011f\u0131n alt k\u0131sm\u0131 olan kolonda ortaya \u00e7\u0131kar.&nbsp;Hirschsprung hastal\u0131\u011f\u0131 ile do\u011fan bebeklerde ba\u011f\u0131rsa\u011f\u0131n belirli k\u0131s\u0131mlar\u0131nda ba\u011f\u0131rsak hareketlerini d\u00fczenleyen rektum ve kolondaki sinir h\u00fccreleri olan ganglion h\u00fccreleri yoktur.&nbsp;Bu h\u00fccrelerin yoklu\u011funa aganglionosis denir.<\/p>\n\n\n\n<p>Bebeklerde bu hastal\u0131k g\u00f6r\u00fcld\u00fc\u011f\u00fcnde kaka yapamazlar.\u00a0Bu durum bebek i\u00e7in \u00e7ok rahats\u0131z edicidir. Kar\u0131nlar\u0131n\u0131n geni\u015flemesine ve \u015fi\u015fmesine neden olabilir, bu da kar\u0131n \u015fi\u015fli\u011fi olarak bilinir.\u00a0Engellenmi\u015f veya t\u0131kanm\u0131\u015f bir ba\u011f\u0131rsak, kolit ad\u0131 verilen kolonun iltihaplanmas\u0131na da neden olabilir.\u00a0Sorun \u00e7\u00f6z\u00fclmezse, bu durum enfeksiyonlara neden olabilir ve sonunda \u00f6l\u00fcme kadar gidebilir. Hirschsprung hastal\u0131\u011f\u0131n\u0131 tedavi etmek i\u00e7in, kolonun etkilenen k\u0131sm\u0131 ameliyatla \u00e7\u0131kar\u0131lmal\u0131d\u0131r.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Hirschsprung hastal\u0131\u011f\u0131na kimler yakalan\u0131r?<\/strong><\/h2>\n\n\n\n<p>Hirschsprung hastal\u0131\u011f\u0131 her 5000 yenido\u011fanda yakla\u015f\u0131k 1 ki\u015fiyi etkiler.\u00a0Hastal\u0131k genetik olabilir, yani bir ebeveyn veya akrabadan aktar\u0131labilir.\u00a0Bu hastal\u0131\u011f\u0131 erkeklerde k\u0131zlara g\u00f6re d\u00f6rt kat daha yayg\u0131nd\u0131r.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Hirschsprung hastal\u0131\u011f\u0131n\u0131n belirtileri nelerdir?<\/strong><\/h2>\n\n\n\n<p>Hirschsprung hastal\u0131\u011f\u0131n\u0131n belirtileri rahats\u0131zl\u0131\u011f\u0131n ciddiyetine g\u00f6re de\u011fi\u015febilir.&nbsp;Genellikle belirtiler ve semptomlar do\u011fumdan k\u0131sa bir s\u00fcre sonra ortaya \u00e7\u0131kar, ancak bazen ya\u015fam\u0131n ilerleyen zamanlar\u0131na kadar belirti g\u00f6stermeyebilir.<\/p>\n\n\n\n<p>Genel olarak, en belirgin durum, yenido\u011fan\u0131n do\u011fumdan sonraki 48 saat i\u00e7inde ba\u011f\u0131rsak hareketine sahip olmamas\u0131d\u0131r.<\/p>\n\n\n\n<p>Yenido\u011fanlarda di\u011fer belirti ve semptomlar \u015funlar\u0131 i\u00e7erebilir:<\/p>\n\n\n\n<ul><li>Kar\u0131n \u015fi\u015fmesi<\/li><li>Ye\u015fil veya kahverengi kusma<\/li><li>Kab\u0131zl\u0131k veya gaz<\/li><li>\u0130shal<\/li><\/ul>\n\n\n\n<p>Daha b\u00fcy\u00fck \u00e7ocuklarda belirtiler ve semptomlar \u015funlar\u0131 i\u00e7erebilir:<\/p>\n\n\n\n<ul><li>\u015ei\u015fmi\u015f g\u00f6bek<\/li><li>Kronik kab\u0131zl\u0131k<\/li><li><a href=\"https:\/\/annelertoplandik.com\/blog\/bebege-gaz-yapan-yiyecekler-neler\/\">Gaz<\/a><\/li><li>Geli\u015fmeme<\/li><li>Yorgunluk<\/li><\/ul>\n\n\n\n<h2 class=\"wp-block-heading\"><strong>Hirschsprung hastal\u0131\u011f\u0131 nas\u0131l tedavi edilir?<\/strong><\/h2>\n\n\n\n<p>\u00c7o\u011fu insan, kolonun sinir h\u00fccrelerinden yoksun k\u0131sm\u0131n\u0131 almak i\u00e7in ameliyatla tedavi edilir.\u00a0Bunun iki yolu vard\u0131r: \u201cbir \u00e7ekme ameliyat\u0131 veya bir ostomi ameliyat\u0131\u201d.<\/p>\n\n\n\n<p>Kesin prosed\u00fcrler her hasta i\u00e7in de\u011fi\u015febilir. Hirschsprung hastal\u0131\u011f\u0131n\u0131n cerrahisi tipik olarak d\u00f6rt ad\u0131m i\u00e7erir:<\/p>\n\n\n\n<ul><li>Bas\u0131nc\u0131 hafifletmek ve d\u0131\u015fk\u0131 ve gaz\u0131n ge\u00e7mesine izin vermek i\u00e7in kolon veya rektumdaki ilk t\u0131kan\u0131kl\u0131\u011f\u0131 temizlemek.<\/li><li>Kolonun aganglionik b\u00f6l\u00fcm\u00fcn\u00fcn (alan eksik ganglion h\u00fccreleri) \u00e7\u0131kar\u0131lmas\u0131.<\/li><li>D\u0131\u015fk\u0131y\u0131 ge\u00e7mek i\u00e7in bir yol olu\u015fturmak i\u00e7in kolonun sa\u011fl\u0131kl\u0131 k\u0131sm\u0131n\u0131 rektuma ba\u011flamak.<\/li><li>Kesi kapat\u0131l\u0131yor.<\/li><\/ul>\n\n\n\n<p>2. ve 3. ad\u0131mda &#8220;\u00e7ekme prosed\u00fcr\u00fc&#8221; denilen i\u015flem yap\u0131l\u0131r.&nbsp;Bu operasyon veya bu tekni\u011fin baz\u0131 varyasyonlar\u0131, Hirschsprung hastal\u0131\u011f\u0131 tedavisinde kullan\u0131lan en yayg\u0131n cerrahi prosed\u00fcrd\u00fcr.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Hirschsprung hastal\u0131\u011f\u0131, kal\u0131n ba\u011f\u0131rsa\u011f\u0131 (kolon) etkileyen ve d\u0131\u015fk\u0131 ge\u00e7irmede sorunlara neden olan bir durumdur.&nbsp;Durum do\u011fumda (konjenital) bebe\u011fin kal\u0131n ba\u011f\u0131rsak kaslar\u0131ndaki eksik sinir h\u00fccrelerinin bir sonucu olarak ortaya \u00e7\u0131kar. Hirschsprung hastal\u0131\u011f\u0131 olan bir yenido\u011fan genellikle do\u011fumdan sonraki g\u00fcnlerde ba\u011f\u0131rsak hareketine sahip olamaz.\u00a0Hafif vakalarda, \u00e7ocukluk \u00e7a\u011f\u0131n\u0131n sonlar\u0131na kadar durum tespit edilemeyebilir.\u00a0Nadiren, bu hastal\u0131k ilk olarak yeti\u015fkinlerde te\u015fhis [&hellip;]<\/p>\n","protected":false},"author":7,"featured_media":2367,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"tdm_status":"","tdm_grid_status":"","footnotes":""},"categories":[38],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Hirschsprung Hastal\u0131\u011f\u0131 Nedir? | Anneler Topland\u0131k<\/title>\n<meta name=\"description\" content=\"Hirschsprung hastal\u0131\u011f\u0131 konjenital bir kusurdur, yani bir ki\u015fi onunla do\u011far.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/annelertoplandik.com\/blog\/hirschsprung-hastaligi-nedir\/\" \/>\n<meta property=\"og:locale\" content=\"tr_TR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Hirschsprung Hastal\u0131\u011f\u0131 Nedir? 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